A Case of Multisystemic Langerhans Cell Histiocytosis in an Adult


  • Chng Chiaw Ling Singapore General Hospital


A 23-year-old female smoker presented in late 2008 with a large left pneumothorax. She had multiple spontaneous pneumothoraces in 2007 which required pleurectomy. A presumptive diagnosis of lymphangioleiomyomatosis (LAM) was made in 2007 after the high-resolution computed tomography (HRCT) of the thorax revealed bilateral interlobular septal thickening and multiple thin walled cystic air spaces without lobar predilection, and with preservation of lung volumes.


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How to Cite

Ling, C. C. (2014). A Case of Multisystemic Langerhans Cell Histiocytosis in an Adult. Journal of the ASEAN Federation of Endocrine Societies, 26(1), 69. Retrieved from https://asean-endocrinejournal.org/index.php/JAFES/article/view/107



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