Langerhans Cell Histiocytosis Presenting as Anterior Neck Mass in a Child:: A Case Report

Kristine Mae Betansos; Melissa Joyanne Cachero; Caridad Santos; Eve Fernandez; Marichu Mabulac; Lorna Abad

doi:10.15605/jafes.038.02.15

Authors

Kristine Mae Betansos Philippine Children's Medical Center, Quezon City, Philippines https://orcid.org/0000-0002-3629-7577
Melissa Joyanne Cachero Philippine Children's Medical Center, Quezon City, Philippines
Caridad Santos Philippine Children's Medical Center, Quezon City, Philippines
Eve Fernandez Philippine Children's Medical Center, Quezon City, Philippines https://orcid.org/0000-0001-5217-529X
Marichu Mabulac Philippine Childrne's Medical Center, Quezon City, Philippines
Lorna Abad Philippine Children's Medical Center

DOI:

https://doi.org/10.15605/jafes.038.02.15

Keywords:

Langerhans Cell Histiocytosis, thyroid, multisystem LCH

Abstract

Thyroid involvement in Langerhans Cell Histiocytosis (LCH) is rare. We report a 10-year-old Filipino male who presented
with a rapidly enlarging goiter. Computed tomography scan showed thyroid and bilateral submandibular masses with
malignant features, pulmonary blebs and hepatic cysts. Ultrasound-guided core needle biopsy findings were consistent with LCH and chemotherapy was initiated. This case demonstrates that LCH should be considered in patients with goiter. Multidisciplinary management is warranted to achieve proper diagnosis and institute timely treatment.

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Author Biographies

Kristine Mae Betansos, Philippine Children's Medical Center, Quezon City, Philippines

Section of Pediatric Endocrinology

Melissa Joyanne Cachero, Philippine Children's Medical Center, Quezon City, Philippines

Section of Pediatric Endocrinology

Caridad Santos, Philippine Children's Medical Center, Quezon City, Philippines

Consultant, Section of Pediatric Endocrinology

Eve Fernandez, Philippine Children's Medical Center, Quezon City, Philippines

Consultant, Section of Pediatric Endocrinology

Marichu Mabulac, Philippine Childrne's Medical Center, Quezon City, Philippines

Consultant, Section of Pediatric Endocrinology

Lorna Abad, Philippine Children's Medical Center

Consultant, Section of Pediatric Endocrinology

Department of Pediatrics, Philippine General Hospital, Manila

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