Transient Pseudohypoaldosteronism in an Infant: A Case Report



pseudohypoaldosteronism, urinary tract infection (UTI), urinary tract anomalies


Transient pseudohypoaldosteronism is strongly linked to urinary tract infections complicating structural urinary tract anomalies. A 3-month-old baby girl with hyponatremia, hyperkalemia and metabolic acidosis associated with urinary tract infection and structural urinary tract anomalies was diagnosed with transient pseudohypoaldosteronism following elevated serum aldosterone and normal 17-hydroxyprogesterone level. Electrolytes normalized with corrections and antibiotic therapy. Clinicians should have a high index of suspicion of transient pseudohypoaldosteronism in an infant presenting with hyponatremia, hyperkalemia and urinary tract infection with or without associated urinary tract anomalies.


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How to Cite

Latt, T. N., Rahman, S. I., & Mohd Nor, N. S. (2018). Transient Pseudohypoaldosteronism in an Infant: A Case Report. Journal of the ASEAN Federation of Endocrine Societies, 33(1), 45. Retrieved from



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