Doege-Potter Syndrome: A Presumptive Case of Metastatic Hemangiopericytoma with Persistent Hypoglycemia in a 27-Year-Old Male


  • Von Lovel Zarra Southern Philippines Medical Center, Davao City, Philippines
  • Kenny Jun Demegillo Southern Philippines Medical Center, Davao City, Philippines
  • May Uyking-Naranjo Southern Philippines Medical Center, Davao City, Philippines
  • Ahmad Domado Southern Philippines Medical Center, Davao City, Philippines



Doege-Potter syndrome, hemangioperictyoma, hypoglycemia


Doege-Potter syndrome (DPS) is a rare paraneoplastic condition characterized by hypoinsulinemic hypoglycemia from a solitary fibrous tumor. The underlying mechanism is the secretion of a prohormone form of insulin-like growth factor II (IGF-II) by the tumor, which causes decreased release of glucose into the circulation. We report the case of a 27-year-old Filipino male with presumptive DPS from a recurrent right temporo-zygomatic hemangiopericytoma (HPC). The complexity of DPS requires a multidisciplinary approach. Early screening for metastases from HPC may prevent the undesirable sequelae of the disease process.



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Author Biographies

Von Lovel Zarra, Southern Philippines Medical Center, Davao City, Philippines

Medical Officer III, Department of Internal Medicine

Kenny Jun Demegillo, Southern Philippines Medical Center, Davao City, Philippines

Medical Specialist, Department of Endocrinology

May Uyking-Naranjo, Southern Philippines Medical Center, Davao City, Philippines

Medical Specialist, Section of Endocrinology, Department of Internal Medicine

Ahmad Domado, Southern Philippines Medical Center, Davao City, Philippines

Department of Internal Medicine


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How to Cite

Zarra, V. L., Demegillo, K. J., Uyking-Naranjo, M., & Domado, A. (2021). Doege-Potter Syndrome: A Presumptive Case of Metastatic Hemangiopericytoma with Persistent Hypoglycemia in a 27-Year-Old Male. Journal of the ASEAN Federation of Endocrine Societies, 36(1), 90–94.



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