Rare Presentation of Right Adrenal Mass

Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia

Keywords: Adrenal mass, Adrenal incidentaloma, Extramedullary hematopoiesis, Thalassaemia, Congenital haemolytic disorder

Abstract

Extramedullary hematopoiesis (EMH) is a rare cause of adrenal mass. We present a 44-year-old woman who has thalassaemia intermedia, referred to Endocrinology clinic for huge adrenal mass. Along with a paraspinal lesion discovered in this patient, the leading diagnosis was EMH. The patient was treated with hypertransfusion and hydroxyurea, which led to a reduction in the size of the right adrenal mass and paraspinal mass.

This case highlights the challenges in managing this rare condition. Although EMH is a rare cause of adrenal mass, the diagnosis must be considered in any patient with a history of a congenital hemolytic disorder, to avoid unnecessary surgical procedures.

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Author Biographies

Poh Shean Wong, Hospital Tuanku Ja'afar Seremban, Malaysia

Endocrine Fellow. Endocrinology Unit, Department of Medicine

Lit Sin Yong , Hospital Tuanku Ja'afar Seremban, Malaysia

Endocrinology Unit, Department of Medicine

Nor Afidah Karim , Hospital Tuanku Ja’afar Seremban

Endocrinology Unit, Department of Medicine

Ee Leng Gan, Hospital Tuanku Ja’afar Seremban

Haematology Unit, Department of Medicine

See Guan Toh , Hospital Tuanku Ja’afar Seremban

Haematology Unit, Department of Medicine

Noor Lita Adam , Hospital Tuanku Ja’afar Seremban

Endocrinology Unit, Department of Medicine

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Published
2021-04-17
How to Cite
Wong, P. S., Yong , L. S., Karim , N. A., Gan, E. L., Toh , S. G., & Adam , N. L. (2021). Rare Presentation of Right Adrenal Mass : Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia. Journal of the ASEAN Federation of Endocrine Societies, 36(1). Retrieved from https://asean-endocrinejournal.org/index.php/JAFES/article/view/969
Section
Case Reports