A Case of Appendiceal Goblet Cell Carcinoid Tumor

Getting it Right under the Microscope

  • Waye Hann Kang University Tunku Abdul Rahman http://orcid.org/0000-0003-3209-7196
  • Norasyikin Abdul Wahab Pusat Perubatan Universiti Kebangsaan Malaysia
  • Nor Azmi Kamaruddin Pusat Perubatan Universiti Kebangsaan Malaysia
Keywords: goblet cell carcinoid, mized neuroendocrine-non-endocrine neoplasm, MINEN, histopathology

Abstract

Goblet cell carcinoid (GCC) is a rare neoplasm of the vermiform appendix and can be mistaken as a typical neuroendocrine tumour (TNET). The natural history of this disease is more aggressive compared to TNETs and requires a more aggressive approach. We report a case of a 37-year-old male who was initially diagnosed with TNET, but subsequently revised as Tang’s A GCC. He underwent appendectomy and right hemicolectomy. Aside from a persistently elevated carcinoembyrogenic antigen (CEA) result, his 18F-fluorodeoxyglucose (FDG) PET/CT and a 68-Gallium DOTATATE PET/CT scan showed no FDG or DOTATATE avid lesions.

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Author Biographies

Waye Hann Kang, University Tunku Abdul Rahman

Lecturer

Department of Medicine, Faculty of Medicine and Health Sciences

Norasyikin Abdul Wahab, Pusat Perubatan Universiti Kebangsaan Malaysia

Department of Medicine

Nor Azmi Kamaruddin, Pusat Perubatan Universiti Kebangsaan Malaysia

Department of Medicine

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Published
2020-04-19
How to Cite
Kang, W. H., Abdul Wahab, N., & Kamaruddin, N. A. (2020). A Case of Appendiceal Goblet Cell Carcinoid Tumor: Getting it Right under the Microscope. Journal of the ASEAN Federation of Endocrine Societies, 35(1). Retrieved from https://asean-endocrinejournal.org/index.php/JAFES/article/view/779